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DeCS
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Descritor Inglês:
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Glutaryl-CoA Dehydrogenase
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Descritor Espanhol:
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glutaril-CoA deshidrogenasa
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Descritor Português:
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Glutaril-CoA Desidrogenase
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Sinônimos Inglês:
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CoA Dehydrogenase, Glutaryl
Dehydrogenase, Glutaryl CoA
Dehydrogenase, Glutaryl-CoA
Dehydrogenase, Glutaryl-Coenzyme A
Glutaryl CoA Dehydrogenase
Glutaryl Coenzyme A Dehydrogenase
Glutaryl-Coenzyme A Dehydrogenase
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Categoria:
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D08.811.682.660.425
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Definição Inglês:
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A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase. |
Nota Histórica Inglês:
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2006(1973)
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Qualificadores Permitidos Inglês:
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Número do Registro:
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50627
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Identificador Único:
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D050770
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Ocorrência na BVS:
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Similar:
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DeCS
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