Pesquisa sobre: GLUTARYL-COA DEHYDROGENASE 
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Descritor Inglês:   Glutaryl-CoA Dehydrogenase 
Descritor Espanhol:   glutaril-CoA deshidrogenasa 
Descritor Português:   Glutaril-CoA Desidrogenase 
Sinônimos Inglês:   CoA Dehydrogenase, Glutaryl
Dehydrogenase, Glutaryl CoA
Dehydrogenase, Glutaryl-CoA
Dehydrogenase, Glutaryl-Coenzyme A
Glutaryl CoA Dehydrogenase
Glutaryl Coenzyme A Dehydrogenase
Glutaryl-Coenzyme A Dehydrogenase  
Categoria:   D08.811.682.660.425
Definição Inglês:   A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase. 
Nota Histórica Inglês:   2006(1973) 
Qualificadores Permitidos Inglês:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DF deficiency DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Número do Registro:   50627 
Identificador Único:   D050770 

Ocorrência na BVS:
 

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